|A.||Scapula is dysplastic|
Omovertebral bone is a usual radiological finding
Glenoid faces downwards
Enlarged scapuloclavicular space
Sprengel’s deformity of the Shoulder:
- Sprengel deformity is a rare congenital disorder in which the shoulder blade (scapula) is too high on one side of the body.
The affected abnormal shoulder blade is also abnormally connected to the spine, often restricting movement of the shoulder
Sprengel deformities usually coexist with other congenital abnormalities, particularly those involving the vertebrae and ribs. An omovertebral bar (fibrous, cartilaginous and/or osseous connection between the scapula and cervical spine) is often present.
It is also commonly associated with hypoplasia or atrophy of regional muscles, and these associated features can cause further misshaping of the shoulder and limitation of shoulder movement.
Patients with Sprengel deformity often have one or more of the following abnormalities and conditions:
- Klippel-Feil syndrome
- spina bifida
- torticollisunderdevelopment of clavicle or humerus